Anti-HADHA Polyclonal Antibody
- 发布日期: 2019-05-13
- 更新日期: 2025-05-13
产品详请
产地 |
北京
|
品牌 |
Solarbio
|
保存条件 |
Store at -20°C. Avoid freeze / thaw cycles.
|
货号 |
K106618P
|
应用范围 |
WB
|
CAS编号 |
|
抗体名 |
Anti-HADHA Polyclonal Antibody
|
克隆性 |
Polyclonal Antibody
|
靶点 |
|
适应物种 |
Human Mouse Rat
|
形态 |
|
宿主 |
Rabbit
|
亚型 |
IgG
|
标识物 |
HADHA;ECHA;GBP;HADH;LCEH;LCHAD;MTPA;TP-ALPHA
|
浓度 |
%
|
免疫原 |
Recombinant protein of human HADHA
|
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.