北京索莱宝科技有限公司
产品展厅
Anti-HADHA Polyclonal Antibody
  • 品牌:Solarbio
  • 产地:北京
  • 货号:K106618P
  • 发布日期: 2019-05-13
  • 更新日期: 2025-05-13
产品详请
产地 北京
品牌 Solarbio
保存条件 Store at -20°C. Avoid freeze / thaw cycles.
货号 K106618P
应用范围 WB
CAS编号
抗体名 Anti-HADHA Polyclonal Antibody
克隆性 Polyclonal Antibody
靶点
适应物种 Human Mouse Rat
形态
宿主 Rabbit
亚型 IgG
标识物 HADHA;ECHA;GBP;HADH;LCEH;LCHAD;MTPA;TP-ALPHA
浓度 %
免疫原 Recombinant protein of human HADHA
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
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